Generalized glycogenosis in Brahman-derived breeds: diagnosis and prevalence in Argentina

Generalized glycogenosis is a lethal autosomal recessive disease caused by a deficient activity of the acidic 1,4-α-glucosidase enzyme and characterized by an accumulation of glycogen within lysosomes. Three mutations in the GAA gene causing bovine generalized glycogenosis have been identified in tw...

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Main Authors: Caffaro, María Eugenia, Raschia, Maria Agustina, Amadio, Ariel, Poli, Mario Andres
Format: info:ar-repo/semantics/artículo
Language:Inglés
Published: Springer 2020
Subjects:
Online Access:https://link.springer.com/article/10.1007%2Fs11250-019-02026-6
http://hdl.handle.net/20.500.12123/6628
https://doi.org/10.1007/s11250-019-02026-6
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author Caffaro, María Eugenia
Raschia, Maria Agustina
Amadio, Ariel
Poli, Mario Andres
author_browse Amadio, Ariel
Caffaro, María Eugenia
Poli, Mario Andres
Raschia, Maria Agustina
author_facet Caffaro, María Eugenia
Raschia, Maria Agustina
Amadio, Ariel
Poli, Mario Andres
author_sort Caffaro, María Eugenia
collection INTA Digital
description Generalized glycogenosis is a lethal autosomal recessive disease caused by a deficient activity of the acidic 1,4-α-glucosidase enzyme and characterized by an accumulation of glycogen within lysosomes. Three mutations in the GAA gene causing bovine generalized glycogenosis have been identified in two cattle breeds, Brahman and Shorthorn. The objective of this study was to evaluate the prevalence of carriers of the E7 mutation in the GAA gene in Argentinean Brahman-derived herds. A total of 930 Braford, 94 Brangus, and 8 Brahman samples were analyzed. The genotyping was done by polymerase chain reaction and restriction fragment length polymorphism (PCR/RFLP). We found that 12.02% (95% CI 12.00-12.04) of the total number of samples received were heterozygous (i.e., carriers) for the E7 mutation, while 12.58% (95% CI 12.56-12.60) of the Braford, 6.38% (95% CI 6.26-6.51) of the Brangus, and 12.50% (95% CI 9.82-15.18) of the Brahman samples were carriers of this loss-of-function allele. Neither breed nor sex were significantly associated to the presence of the mutation. The prevalence informed in this study is similar to the average prevalence reported for Australian Brahmans. The finding of heterozygous animals suggests that breeders and insemination centers should continue screening their herds to minimize the dissemination of this deleterious allele.
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institution Instituto Nacional de Tecnología Agropecuaria (INTA -Argentina)
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spelling INTA66282020-01-07T16:01:09Z Generalized glycogenosis in Brahman-derived breeds: diagnosis and prevalence in Argentina Caffaro, María Eugenia Raschia, Maria Agustina Amadio, Ariel Poli, Mario Andres Glycogenolysis Lysosomes Cattle Breeds Diagnostic Techniques Mutation Breeding Carrier State Glicogenolisis Lisosomas Raza Bovina Técnicas de Diagnosis PCR Argentina Mejoramiento por Mutación Estado Portador Raza Brahman Raza Shorthorn Generalized glycogenosis is a lethal autosomal recessive disease caused by a deficient activity of the acidic 1,4-α-glucosidase enzyme and characterized by an accumulation of glycogen within lysosomes. Three mutations in the GAA gene causing bovine generalized glycogenosis have been identified in two cattle breeds, Brahman and Shorthorn. The objective of this study was to evaluate the prevalence of carriers of the E7 mutation in the GAA gene in Argentinean Brahman-derived herds. A total of 930 Braford, 94 Brangus, and 8 Brahman samples were analyzed. The genotyping was done by polymerase chain reaction and restriction fragment length polymorphism (PCR/RFLP). We found that 12.02% (95% CI 12.00-12.04) of the total number of samples received were heterozygous (i.e., carriers) for the E7 mutation, while 12.58% (95% CI 12.56-12.60) of the Braford, 6.38% (95% CI 6.26-6.51) of the Brangus, and 12.50% (95% CI 9.82-15.18) of the Brahman samples were carriers of this loss-of-function allele. Neither breed nor sex were significantly associated to the presence of the mutation. The prevalence informed in this study is similar to the average prevalence reported for Australian Brahmans. The finding of heterozygous animals suggests that breeders and insemination centers should continue screening their herds to minimize the dissemination of this deleterious allele. Instituto de Genética Fil: Caffaro, Marí­a Eugenia. Instituto Nacional de Tecnología Agropecuaria (INTA). Instituto de Genética; Argentina Fil: Raschia, Maria Agustina. Instituto Nacional de Tecnología Agropecuaria (INTA). Instituto de Genética; Argentina Fil: Amadio, Ariel. Instituto Nacional de Tecnología Agropecuaria (INTA). Estación Experimental Agropecuaria Rafaela; Argentina. Consejo Nacional de Investigaciones Científicas y Técnicas; Argentina Fil: Poli, Mario Andres. Instituto Nacional de Tecnología Agropecuaria (INTA). Instituto de Genética; Argentina 2020-01-07T15:55:32Z 2020-01-07T15:55:32Z 2019-08 info:ar-repo/semantics/artículo info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion https://link.springer.com/article/10.1007%2Fs11250-019-02026-6 http://hdl.handle.net/20.500.12123/6628 1573-7438 https://doi.org/10.1007/s11250-019-02026-6 eng info:eu-repograntAgreement/INTA/PNBIO/1131033/AR./Genómica y biotecnología aplicada a la cría animal. info:eu-repo/semantics/restrictedAccess application/pdf Springer Tropical Animal Health and Production : 1–6 (Agosto 2019)
spellingShingle Glycogenolysis
Lysosomes
Cattle Breeds
Diagnostic Techniques
Mutation Breeding
Carrier State
Glicogenolisis
Lisosomas
Raza Bovina
Técnicas de Diagnosis
PCR
Argentina
Mejoramiento por Mutación
Estado Portador
Raza Brahman
Raza Shorthorn
Caffaro, María Eugenia
Raschia, Maria Agustina
Amadio, Ariel
Poli, Mario Andres
Generalized glycogenosis in Brahman-derived breeds: diagnosis and prevalence in Argentina
title Generalized glycogenosis in Brahman-derived breeds: diagnosis and prevalence in Argentina
title_full Generalized glycogenosis in Brahman-derived breeds: diagnosis and prevalence in Argentina
title_fullStr Generalized glycogenosis in Brahman-derived breeds: diagnosis and prevalence in Argentina
title_full_unstemmed Generalized glycogenosis in Brahman-derived breeds: diagnosis and prevalence in Argentina
title_short Generalized glycogenosis in Brahman-derived breeds: diagnosis and prevalence in Argentina
title_sort generalized glycogenosis in brahman derived breeds diagnosis and prevalence in argentina
topic Glycogenolysis
Lysosomes
Cattle Breeds
Diagnostic Techniques
Mutation Breeding
Carrier State
Glicogenolisis
Lisosomas
Raza Bovina
Técnicas de Diagnosis
PCR
Argentina
Mejoramiento por Mutación
Estado Portador
Raza Brahman
Raza Shorthorn
url https://link.springer.com/article/10.1007%2Fs11250-019-02026-6
http://hdl.handle.net/20.500.12123/6628
https://doi.org/10.1007/s11250-019-02026-6
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AT amadioariel generalizedglycogenosisinbrahmanderivedbreedsdiagnosisandprevalenceinargentina
AT polimarioandres generalizedglycogenosisinbrahmanderivedbreedsdiagnosisandprevalenceinargentina